Congenital Heart Block with Long QT Interval
Report:
Sinus rhythm 100 - 110/min
Third degree AV block
Junctional escape rhythm 48/min
VEB
SVEB
Prolonged QT interval 0.60”
QTc 0.53”
Comment:
This case has been reported73.
While it is not possible to exclude post-syncopal QT prolongation in this setting, it is as likely that AV block is part of the Romano-Ward syndrome. Whatever the cause, it has the capacity to facilitate torsade de pointes tachycardia. She had several runs while in ICU, followed by ventricular standstill.
Her convulsions and syncope were due to the torsades rather than AV block.
Both AV block and long QT interval syndromes can be treated by pacing. The therapeutic implications of their unusual conjunction in this case is that the pacing rate should be set higher, because it is the long QT interval causing the symptoms.
A representative strip of one of her syncopal attacks (without seizures) is shown below (Fig 114a).
If you have any suggestions for or feedback on this report, please let us know.
Hi, can we chat about some terms and conditions?
The library and it's records are licensed under the Creative Commons Attribution 4.0 International license.
You are free to:
- Share — copy and redistribute the material in any medium or format for any purpose, even commercially.
- Adapt — remix, transform, and build upon the material for any purpose, even commercially.
- The licensor cannot revoke these freedoms as long as you follow the license terms.
Under the following terms:
- Attribution — You must give appropriate credit , provide a link to the license, and indicate if changes were made . You may do so in any reasonable manner, but not in any way that suggests the licensor endorses you or your use.
- No additional restrictions — You may not apply legal terms or technological measures that legally restrict others from doing anything the license permits.
By clicking agree below, you are agreeing to adhere to CC BY 4.0.