Romano-Ward Syndrome

Report:

Sinus rhythm 54 - 64/min

Prolonged QT interval 0.56”

Upper limit of normal for rate 57/min 0.41”

Comment:

The only abnormality is the long QT interval. The Romano121-Ward122 syndrome is similar to Jervell and Lange-Nielsen syndrome123, but there is no deafness. Syncope and death are due to torsade de pointes tachycardia. The two are, however, distinct genetically.

Portion of the medical report accompanying the patient is shown below (Fig 167a).

Unfortunately he slipped through our hands in Canberra and went to Melbourne, before another ECG could be secured. Rara avis.

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