LVH: COCM in Tuberous Sclerosis
Report:
Sinus rhythm 148/min
SVEBs, some aberrant
Left ventricular hypertrophy with ST/T changes
Comment:
In epiloia – sclérose tuberéuse de Bourneville – LVH is mostly seen with evidence of CCF, like in this infant with fractional shortening of only 13% (normal >29%). He was started on carvedilol for COCM.
It is less well known that large intramural rhabdomyomata may have electrical activity and produce striking LVH with preserved LV function26. Most regress over time, with corresponding normalisation of the ECG.
If you have any suggestions for or feedback on this report, please let us know.
Hi, can we chat about some terms and conditions?
The library and it's records are licensed under the Creative Commons Attribution 4.0 International license.
You are free to:
- Share — copy and redistribute the material in any medium or format for any purpose, even commercially.
- Adapt — remix, transform, and build upon the material for any purpose, even commercially.
- The licensor cannot revoke these freedoms as long as you follow the license terms.
Under the following terms:
- Attribution — You must give appropriate credit , provide a link to the license, and indicate if changes were made . You may do so in any reasonable manner, but not in any way that suggests the licensor endorses you or your use.
- No additional restrictions — You may not apply legal terms or technological measures that legally restrict others from doing anything the license permits.
By clicking agree below, you are agreeing to adhere to CC BY 4.0.